New research reveals a significantly higher rate of hearing loss in children and adults with sickle cell disease (SCD) and sickle cell traits (SCT). The results spotlight the need for awareness and action in populations most affected by SCD.
The context: SCD is most common in people with ancestry from Africa, the Mediterranean, South Asia, and parts of Hispanic America.
- SCD affects 1 in 365 Black babies and 1 in 16,300 Hispanic babies in the US.
- A recent study showed that nearly 94% of people hospitalized for SCD in the US were Black, while only 5% were Hispanic and 2% were White.
- Sickle cell traits (SCT): People with sickle cell traits typically live with no medical problems related to SCT. However, under extreme conditions such as severe dehydration or high-intensity physical activity, people with SCT can experience health issues, including muscle breakdown, reduced blood supply to the spleen, and eye pressure.
- SCT is considerably more prevalent: About 1 in 13 Black or African-American babies are born with SCT vs 1 in 365 babies for SCD.
Why it matters
SCD and SCT significantly increase the risk of hearing loss in children and adults.
- Early detection and intervention are crucial.
Study results
Hearing loss is linked to SCD and SCT in the following ways:
- Prevalence: Children and adults with SCD and SCT were 2-3 times more likely to experience hearing loss than those with normal hemoglobin.
- Earlier onset: Hearing loss may start earlier in life for children with SCD, highlighting the need for early screening.
- Severity: People with SCD had a stronger association with hearing loss than those with SCT.
How it works
- Sickle-shaped red blood cells in SCD can restrict blood flow, potentially damaging the cochlea (hearing organ).
- Vaso-occlusive crises (VOCs), a hallmark of SCD, can further harm the cochlea and lead to hearing loss.
- VOCs are a common and painful complication of SCD. It occurs when sickled red blood cells block blood flow. VOCs have a variety of causes, such as cold temperatures, dehydration, infection, and stress. Standard treatments include pain-relieving medications, oxygen therapy, fluids, and sometimes blood transfusions.
The way to win
- Annual hearing screenings: Early detection is essential for children and adults with SCD and SCT.
- Early intervention: If hearing loss is identified, prompt treatment (hearing aids, therapy) significantly improves outcomes.
- Raise awareness: Share this information with your family, friends, and healthcare providers.
Schedule a free hearing screening
Hearing loss is gradual and not benign. Untreated, it increases your risk of social isolation, falling, and dementia.
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